MNJ30-001

images/MNJ-P-OSCE 30. Gastroenterology_page_8_Picture_7.jpeg

  1. Identify the radiological imaging
  2. Mention two precautions to be taken prior to doing this imaging.

Answer

No model answer in source material.


MNJ30-002

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images/MNJ-P-OSCE 30. Gastroenterology_page_9_Picture_2.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_9_Picture_7.jpeg

  1. What 1s this modality of investigation?
  2. Name one common indication
  3. Diagnosis.
  4. Whatis the clinical diagnosis?
  5. What 1s the requirement of echo before surgery?
  6. What are poor surgical prognostic factors?

Answer

No model answer in source material.


MNJ30-003
An 8-year-old female child Ritu presents with acute pain abdomen, fever with vomiting from 12 hours child is looks dehydrated on examination with tenderness at right iliac fossa, X-ray was:

images/MNJ-P-OSCE 30. Gastroenterology_page_9_Picture_14.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_10_Picture_2.jpeg

  1. What 1s clinical diagnosis?
  2. What does X-ray show?
  3. USG criteria for disease.
  4. Most specific sign in clinical examination.
  5. Investigation of choice and gold standard

Answer

No model answer in source material.


MNJ30-004

images/MNJ-P-OSCE 30. Gastroenterology_page_10_Picture_7.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_10_Picture_8.jpeg

  1. Describe the sign and its causes ot image A and B
  2. Association with syndrome with image A.
  3. Associate anomaly with image A.

Answer

No model answer in source material.


MNJ30-005
A 11-year-old male child Neeraj presents with constipation since birth, mother gave history of delayed passage of meconium:

images/MNJ-P-OSCE 30. Gastroenterology_page_10_Picture_15.jpeg

  1. What 1s this study, and what is interpretation?
  2. Diagnosis
  3. How will you differentiate it from functional constipation?
  4. Investigation of choice
  5. Treatment

Answer

No model answer in source material.


MNJ30-006
**(Very Important):

images/MNJ-P-OSCE 30. Gastroenterology_page_11_Picture_8.jpeg

  1. What is the radiological investigation?
  2. What sign 1s demonstrated?
  3. What is the diagnosis?
  4. What is the commonest age group in which the following condition occurs?
  5. What are the other conditions associated with this abnormality?

Answer

No model answer in source material.


MNJ30-007
**

images/MNJ-P-OSCE 30. Gastroenterology_page_11_Picture_12.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_12_Picture_2.jpeg

  1. Write down name of all three diagnosis study.
  2. Diagnosis all three conditions.

Answer

No model answer in source material.


MNJ30-008

images/MNJ-P-OSCE 30. Gastroenterology_page_12_Picture_6.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_12_Picture_7.jpeg

  1. Identify these two images and give the diagnosis.
  2. How will you differentiate tracheal FB from esophagus FB by X-ray?

Answer

No model answer in source material.


MNJ30-009
** A 4-day-old neonate baby of Anita came with complaints of not pass stool since birth, imaging study was done:

images/MNJ-P-OSCE 30. Gastroenterology_page_12_Picture_12.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_13_Picture_2.jpeg

  1. What 1s diagnosis by this image?
  2. What 1s associated condition and what is responsible gene for that?
  3. What 1s characteristic finding in dilated segment during operung of intestine during laparotomy?

Answer

No model answer in source material.


MNJ30-010

images/MNJ-P-OSCE 30. Gastroenterology_page_13_Picture_8.jpeg

  1. Identify the condition.
  2. Write down the classical triad.
  3. Classical barium enema finding.
  4. Treatment

Answer

No model answer in source material.


MNJ30-011
A 14-year-old girl has a 2-month history of diarrhea. She has lost 10 kg in weight. On examination, she looks rather pale; the abdominal examination is unremarkable. She has a barium enema examination. This X-ray is taken from her barium enema series. Examine the film and then answer the questions:

images/MNJ-P-OSCE 30. Gastroenterology_page_13_Picture_14.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_14_Picture_2.jpeg

  1. What abnormal features are shown on this X-ray?
  2. What 1s the diagnosis?
  3. What complications can develop? (Write any 4)
  4. Drugs to treat this condition.

Answer

No model answer in source material.


MNJ30-012
A baby born at term weight: 3.6 kg, was on exclusive breastfeeding for 41/2 months when solid foods were introduced. Was sent to hospital at 8 months of age with history of poor weight gain, intermittent diarrhea, vomiting and irritability. On admission, she was pale with abdominal distension and mild wasting. Her lab reports Hb: 9, WBC 9000, platelet: 4,70,000, Na: 137, K: 5.3, urea 6.6, sweat test is normal:

images/MNJ-P-OSCE 30. Gastroenterology_page_14_Figure_14.jpeg

  1. What is the most likely diagnosis?
  2. Write confirmatory investigation (gold standard).
  3. What treatment was done on admission (refer the growth chart)?
  4. Write yes or no depending upon whether the following foods are permitted for a child suffering from this condition.
    a. Cornflakes
    c. Sago (sabudana)
    b. Maggi noodles
    d. Oats cereal

Answer

No model answer in source material.


MNJ30-013

images/MNJ-P-OSCE 30. Gastroenterology_page_14_Picture_19.jpeg

  1. What is the diagnosis?
  2. What is the embryologic basis of these defects?
  3. In an otherwise healthy child, when are these defects repaired?

Answer

No model answer in source material.


MNJ30-014

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  1. Identify the instrument
  2. What are the indications for its use?
  3. Whatis the mecharusm of its action?

Answer

No model answer in source material.


MNJ30-015

  1. Write down model menu for mid-day school meal.
  2. According to National Institute of Nutrition minimum number of feeding days in a year should be (mention days) to have desired impact on the children.

Answer

No model answer in source material.


MNJ30-016
A 2-year-old child is evaluated 18 months after an unsuccessful Kasai procedure to treat extrahepatic biliary atresia. He is jaundiced and has signs of cirrhosis and portal hypertension. He is drowsy, has an ataxic gait and shows no deep tendon reflexes. What has led to this neuromuscular disorder?

Answer

No model answer in source material.


MNJ30-017

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images/MNJ-P-OSCE 30. Gastroenterology_page_15_Picture_16.jpeg

  1. Identify these two USG film and write down the ultrasound critena for diagnosis of this disease.
  2. What is medical treatment available?
  3. Triad of gastric volvulus.

Answer

No model answer in source material.


MNJ30-018
Case scenario

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  1. An 18-month-old boy is receiving augmentin for otitis media. Now he has diarrhea and a diaper rash. There is no fever or vomiting.
  2. A 3-year-old male has temperature of 103°F and shaking chills versus febrile seizure. He and other children in his daycare have had diarrhea and fevers. He has had blood in the stool.
  3. A 12-year-old female has had diarrhea, bloating and gas. She often notices some abdominal pain in the late mornings and early afternoon. She has not noticed blood in her stool.

Answer

No model answer in source material.


MNJ30-019
A 13-year-old boy develops right upper-quadrant pain and fever with chills and rigors. An abdominal ultrasound reveals: Hyperechoic liver parenchyma. Dilatation of several intrahepatic bile ducts, few bilateral renal cysts:

  1. What is the diagnosis?
  2. What is the cause of fever with chills in this case?
  3. What are the components of this disease/syndrome?
  4. Which gene has been implicated for the above?

Answer

No model answer in source material.


MNJ30-020
Mention five differences between osmotic and secretory diarrhea.

Answer

No model answer in source material.


MNJ30-021
With regard to the hormone-secreting diarrhea answer the following:

  1. Mention 5 hormones involved in it.
  2. Mention the disease associated with each of those hormones.
  3. Mention one specific treatment for each of those mentioned above

Answer

No model answer in source material.


MNJ30-022

  1. Mention three types of progressive familial intrahepatic cholestasis, with the defect in each of them.
  2. Mention the dosage of fat soluble vitamins required for supplementing in a child with prolonged cholestasis of infancy

Answer

No model answer in source material.


MNJ30-023

  1. Mention five conditions that present a clinical/pathologic picture resembling Reye syndrome.
  2. Write down clinical stages of Reye syndrome

Answer

No model answer in source material.


MNJ30-024
Mention five patterns of hepatic drug injury with one example for each.

Answer

No model answer in source material.


MNJ30-025
Identify images A and B.

images/MNJ-P-OSCE 30. Gastroenterology_page_16_Picture_24.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_16_Picture_25.jpeg

Answer

No model answer in source material.


MNJ30-026
A10-day-old neonate presented with lethargy, feed refusal and abdominal distension. He was on formula-feed and born as 31 weeks preterm:

images/MNJ-P-OSCE 30. Gastroenterology_page_17_Picture_5.jpeg

  1. What stage of NEC 1s depicted in the X-ray?
  2. Whats the radiological feature of bell stage I] NEC?
  3. Name two more conditions associated with pneumatosis intestinalis.

Answer

No model answer in source material.


MNJ30-027
A 5-week-old infant presented with cholestatic but also have swelling in the left thigh that is tender:

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images/MNJ-P-OSCE 30. Gastroenterology_page_18_Picture_2.jpeg

  1. Whatis the likely cause of fracture femur in this case?
  2. How can this complication be prevented?
  3. How do you manage pruritus in these patients?
  4. An infant with cholestasis, triangular facies, and a pulmonic stenosis murmur is likely to have what syndrome?

Answer

No model answer in source material.


MNJ30-028
A two-hour-old neonate presented with severe respiratory distress since birth:

images/MNJ-P-OSCE 30. Gastroenterology_page_18_Picture_7.jpeg

  1. Diagnosis
  2. What are the embryologic events that lead to this development?
  3. What are three causes of respiratory distress in a baby born with this condition?

Answer

No model answer in source material.


MNJ30-029
See the image below and answer the following questions.

| 422 OSCE Clinical Pediatrics |

images/MNJ-P-OSCE 30. Gastroenterology_page_18_Picture_13.jpeg

  1. What 1s the diagnosis?
  2. What 1s the differential diagnosis?
  3. What are the associated anomalies?
  4. What 1s the management?

Answer

No model answer in source material.


MNJ30-030
A7-year-old girl with strong family history of chronic fatal liver disease presents with features of hemolysis. She has complaints of abnormal movement of hand and jaundice since last 7 days:

  1. List one clinical examination which may give the diagnosis.
  2. State most probable group of etiology based on answer to question '1'
  3. List three most important tests for diagnosis with values
  4. Qutline the management of this child.

Answer

No model answer in source material.


MNJ30-031
Match the following:

  1. Secretory diarrhea—thyrotoxicosis
  2. Osmotic diarrhea—cholera
  3. Increase mobility—lactate deficiency
  4. Decrease mobility—celiac disease
  5. Decrease surface area—blind loop

Answer

No model answer in source material.


MNJ30-032

  1. Write down 4 metabolic causes of constipation.
  2. Write down 4 complicahons of vomiting.
  3. Calculate stool anion gap
  4. What 1s importance of stool anion gap?

Answer

No model answer in source material.


MNJ30-033

images/MNJ-P-OSCE 30. Gastroenterology_page_19_Picture_25.jpeg

  1. Identify this mage
  2. Write down its classical / clinical feature.
  3. Whats this? Syndrome/sequence / malformation.
  4. Write two more examples of similar genetic pattern
  5. What 1s strickler syndrome?

Answer

No model answer in source material.


MNJ30-034
True/False about celiac disease:

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images/MNJ-P-OSCE 30. Gastroenterology_page_20_Picture_2.jpeg

  1. Glutenins, hordems, secalins are well known tnggers
  2. HLA DQ6 association.
  3. Short stature is most common manifestation.

Answer

No model answer in source material.


MNJ30-035
A 6-year-old male child Mahapatra presents with ataxia, foul smelling bulky stool from last 30 days, and poor performance in school. Blood triglyceride level is 15 mg/dl:

  1. Whats diagnosis of this condition?
  2. What will you find in retinal examination and peripheral blood film?
  3. Which nervous system parts affect in this disease?
  4. Whats treatment?

Answer

No model answer in source material.


MNJ30-036
Match the following in view of food poisoning:

  1. After 6 hours of ingestion of fned rice with meat present with vomuting.
  2. After 2 days of ingestion of unpasteurize milk present with fever and bloody stool.
  3. After 24 hours of ingestion of egg and milk present with fever, diarrhea
  4. After 6 hours of ingestion of salad in marriage present with vomiting and diarrhea but no fever.

Answer

No model answer in source material.


MNJ30-037
Match the following stool test:

  1. Alpha 1 antitrypsin—increase intestinal permeability.

Answer

No model answer in source material.


MNJ30-038
This is the X-ray of 1-day-old child with distension of abdomen:

images/MNJ-P-OSCE 30. Gastroenterology_page_20_Picture_32.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_21_Picture_2.jpeg

  1. Whats the investigation known as, and what 1s the diagnosis?
  2. Whats the treatment?
  3. True/ False:
  4. Low lesion is associated with perineal fistula and well-formed buttock.
  5. Palmar erethyma, spider navi
  6. Leukonychia
  7. Dupuytren contracture
  8. Fetor hepaticus
  9. Parotid swelling

Answer

No model answer in source material.


MNJ30-039
A 10-year-old male child presents with jaundice, irritability, poor school performance and severe anemia. On examination, child has tremor and chorea like movement

ABsAg Anti-HBe Igm Antti HBc Anti-HBsAg
Be + - = =
b. + + - -
é = = = +
d. a - + -
e. - - + +

©.42. Match the following about hepatitis:

  1. What 1s probable diagnosis of this condition?
  2. What are endocrinal manifestations?
  3. What is gold standard test?
  4. Name 4 drug uses in treatment?
  5. What 1s cause of anemia in this patent?

Answer

No model answer in source material.


MNJ30-040
A mother of two children came to you for advice as she is going to visit another country for 4 months where hepatitis A infection is very prevalent, her older child is 3-year-old and younger one is 9 months advice him about prevention of hepatitis A.

Answer

No model answer in source material.


MNJ30-041
A 7-month-old female baby presented with persistent cough, failure to gain weight and bulging mass from his rectum. Kindly see the image and answer the following question?

ANSWERS

Ans. 1. 1. ERCP

Benificiary should attend school for 20 days/month. Provides 300 calories and 8-12 g protein per day

Ans. 17. Vitamin E deficiency.

Ans. 21.

Osmotic Secretory
Volume <200 ml /day >200 ml /day
Response to fasting Diarrhea stops Continued purging
Stool Na <70 mEq/L >70 mEq/L
Reducing substances Positive Negative
Stool pH <5 >6

Ans. 22. Diarrhea caused by hormone secreting tumors

Seratonin: Carcinoid—somatostatin analogues

Gastrin Gastrinoma—tumor resechon

Histamine: Mastocytoma—cromolyn, steroids, resechon Calcitonin, VIP—medullary carcinoma—thyroidectomy

Catecholamines—ganglioneuroma, pheochromocytoma—oa-blockade, resection

Somatostatin. somatostatinoma—resechon

VIP: VIPoma—somatostatin analogues, resechon

Ans. 23.1. PFIC type Unknown

PFIC type II: Deficient canalicular bile salt transport

PFIC type III Deficient canalicular phosphatidylcholme transport

Vitamin E 50-400 IU /day as alpha tocopherol

Vitamin D 5000-8000 IU/day

Vitamin K 2.5-5.0 mg every other day as menadione

Ans. 24.1. Metabolic diseases

Ans. 25,

Pattern/disease Drug
Centrilobular necrosis Acetaminophen, holothane
Microvesicular steatosis Valproic acid
Fibrosis Methotrexate
Cholestasis Chlorpromazine, erythromycin
Biliary sludge Ceftriaxone
Veno-occlusive disease Busulfan, cyclophosphamide
Portal and hepatic vein thrombosis Estrogens and androgens

Ans. 26. Image A: Giardia lamblia Image B Enterobius vermicularis—eggs

Ans. 27.1. NEC stage II

Trisomies

Congenital cardiac anomalies

. Cover defect with sterile draping

Fluid replacement

Early surgical correction

Ans. 31.1. Kayser-Fleischer rings

Ans. 32. Match the following:

Ans. 35.1. T 1

Campylobacter Staphylococcus Noe N

Ans. 38.1. Protein loss

Ans. 39.1.

Invertogram, anal atresia 2. Low—dilatation, high—colostomy

Ans. 40. 1. Increase estrogen 2. Low albumin

Ans. 41.* Must know everything about Wilson disease

. Carrier 2. Acute infechon

. Vaccinated 4. Chronic infection

. Past infection (recovered)

Ans. 43. See Table 30 1

Table 30.1: Hepatitis A virus prophylaxis
Age Preexposure prophylaxis (Travelers ta Endemic Regions)
Expected Exposure Duration
Dase
<1 year of age
21 year of age
<3 months
3-5 months
Long-term (>5 months)
Healthy host
Immunocompromised host, or one with chronic
liver disease or chronic health problems
Ig 0.02 ml/kg
Ig 0.06 ml/kg
Ig 0.06 ml/kg at departure and
every 5 mo thereafter
HAV vaccine
HAV vaccine and Ig 0.02 ml/kg
Exposure Postexposure Proplnyjlaxis*
Recommendations
#2 wk since exposure
>2 wk since exposure
<1 year-old: Ig 0.02 ml/kg
and HAY vaccine
None
Immunocompromised host, or host with chornic health problems: lg 0.02 mL/kg
>1 year and healthy host HAV vaccine, lg remains optional
Sporadic non-household or close contact exposure: Prophylaxis not indicated*

*Decision for prophylaxis in non-household contacts should be tailored to individual exposure and risk Ig Immunoglobulin.

images/MNJ-P-OSCE 30. Gastroenterology_page_21_Picture_22.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_22_Picture_2.jpeg
images/MNJ-P-OSCE 30. Gastroenterology_page_24_Picture_2.jpeg

  1. Whats the possible diagnosis?
  2. What is possible pathogenesis?
  3. What 1s pathophysiology?
  4. How can we screen this disease m neonatal period?
  5. Indication
  6. Sphincter of Odii dysfunction
  7. Indication
  8. Excessive drooling, chocking
  9. To rule out associated congenital heart diseases right-sided aorta
  10. Gap beetween ends is >3 cm, weight <1500 g
  11. Appendicolith (stone in appendix)
  12. Tenderness at RLQ
  13. USG, CT scan is gold standard
  14. Down syndrome
  15. Annular pancreas
  16. Hirschsprung's disease
  17. Rectal biopsy-but that should be taken 2 cm above the dentate line
  18. Pull through procedure
  19. 2nd part of duodenum dilated and there was passage of very little barium across stricture, giving the classic "cork-screw" appearance 3rd and 4th part of duodenum and proximal jejunal loops were on right side of spine
  20. Malrotation with volvulus
  21. In 80% in first 2 months
    b. T99 pertechnate scan
  22. a. Bılıary atresia
    b. Meckel diverticulum
    c. GERD
  23. Pain, palpable sausage shape mass, currant jelly stool
  24. Filling defect or cupping
  25. Ulcerative colitis
  26. Complications
    a. Cornflakes: Yes
    b. Maggi noodles: No
    d. Oats cereal No
    e. Bajara roti: Yes
  27. Oral or IV atropine sulphate (Nelson).
  28. Gastric volvulus presents as a triad of a sudden onset of severe epigastric pain, intractable retching with emesis, and inability to pass a tube into the stomach
  29. IgA deficiency, cystic fibrosis
  30. Antibiotic induced diarrhea, viral diseas
  31. Shigella, viral infection
  32. Lactose intolerance
  33. Ans. 20.1. Caroli's syndrome
  34. . Cholangitis
  35. . Intra-hepatic ductal ectasia AR polycysthe kidney disease
  36. PKHD, gene
  37. Climcal staging of Reye syndrome
  38. Pneumoperitoneum
  39. Any two of the following Hirschsprung's disease, pseudomembranous enterocolitis, neonatal ulcerative colits, ischemic bowel disease
  40. Replace 5,000-8,000 U/d of D2, or 3-5 mg/kg/d of 25-hydroxycholecaleiferol
  41. Urosodeoxycholic acid 15-20 mg/kg/day
  42. Alagille syndrome (arteriohepatic dysplasia)
  43. The posterolateral portion of the diaphragm has remained open between the ninth and tenth weeks of gestation as a result the viscera will pass into the chest, and a CDH will result.
  44. a. Mechanical compression of the lungs from the hermated viscera
    b. Pulmonary hypoplasia from compression of the developing lungs m ufero
  45. Omphalocele
  46. Beckwith-Wiedeman
  47. Wilson disease
  48. Diagnostic tests
    a. Serum ceruloplasmin <200 mg/L
    b. Urinary copper >100 pg/day
  49. Management
    a. Restrict copper intake
    b. Chelation with penicillamine
    d. Liver transplant
  50. Secretory diarrhea—cholera
  51. Osmotic diarrhea—lactate deficiency
  52. Increase mobility—Thyrotoxicosis
  53. Decrease mobility—blind loop celiac disease
  54. Decrease surface area—celiac disease
  55. Mallory-Weiss tear, esophagits, shock, dyselectrolytemia
  56. Stool anion gap = stool osmolality—2 (stool Na* stool K) 290 — 2 (40 + 50) = 110
  57. If stool anion gap 1s <100 = secretory diarrhea >100 = osmotic diarrhea
  58. F(DOQS8)
  59. F. Anemia is most common extraintestinal manifestation
  60. T
  61. F (also present in many diseases)
  62. T (see Nelson)
  63. Cerebellum, basal ganglia, posterior column
  64. Salmonella
  65. Pancreatic insufficiency
  66. Fibrosis of aponeurosis due to free radical injury
  67. Mutation in CFTR (cystic fibrosis transmembrane conductance regulator) gene at chromosome 7

Answer

No model answer in source material.