MNJ33-001
** See the X-ray image and answer the following questions.

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] Cardiology 459 |

images/MNJ-P-OSCE 33. CVS_page_1_Picture_8.jpeg
images/MNJ-P-OSCE 33. CVS_page_1_Picture_17.jpeg

  1. What was the lesion?
  2. What was the procedure carried out?
  3. What are the complications?

Answer

No model answer in source material.


MNJ33-002
A 2-day-old neonate, birth weight: 3.1 kg, on examination, cyanosis +, soft murmur +, single 52. On investigation, hypoxia and acidosis present, chest X-ray shows normal cardiac size:

  1. What 1s most likely diagnosis?
  2. What is the emergency therapy?
  3. Whats the dosage and complications of the drug?

Answer

  1. Duct dependent cyanotic heart disease (most common: D-TGA with intact IVS/ pulmonary atresia with intact IVS)

Systenuc hypotension and apnea are the most common complications.


MNJ33-003
A term infant suddenly develops cardiac failure in the first week of life. The infant was pink, his pulses were collapsing but there is no cardiac murmur. His X-ray showed cardiomegaly. His echo showed normal heart and normal great vessels. His PDA was closed:

  1. What 1s the diagnosis?
  2. What other investigations will be indicated?

Answer

AV fistula


MNJ33-004
See the X-ray image below and answer the following questions.

images/MNJ-P-OSCE 33. CVS_page_2_Picture_12.jpeg

  1. What 1s the diagnosis?
  2. Whats this sign called?
  3. What are structures that cause this appearance in this condition?

Answer

oe Ber Total anomalous pulmonary venous draimage—supracardiac type

Dilatation of both the left and nght innominate veins and mght SVC producing the classical snowman of figure of 8 appearance.

Superior mediastinum is enlarged secondary to right SVC, innominate artery and ascending verhecal vein.


MNJ33-005
1-day-old infant appears dusky during feeding. O, is administered via nasal cannula, and 2 hours later she develops tachypnea. Findings include: HR—170 beats/min; RR—80/ min; R arm BP—48/30 mm Hg; R leg BP—52/32 mm Hg; and pulse oximetry, 90% on oxygen:

  1. Ifthe diagnosis is HLHS describe physical findings of pulse, murmur, precordium and 82.
  2. What was wrong in the management in the above scenario?
  3. Mention 5 CHD presenting in the first week of life
  4. Emergency management.

Answer

  1. HLHS Duct dependent lesion—signs of shock, poor pulses and metabolic acidosis, as systemic perfusion deteriorates, thereby depriving the systemic circulation of adequate perfusion. Hyperdynamic precordium and a loud, even palpable single loud P2 (52), no murmur

MNJ33-006
A 5-day-old infant born at 31 weeks' gestation is on ventilatory support. He has a grade 2 holosystolic murmur that extends the second heart sound. Pulses are bounding. Precordial palpation is hyperdynamic. Echocardiography reveals a large patent ductus without other ductal-dependent congenital lesions:

  1. When would one suspect PDA in preterm clinically
  2. Mention 3 complications of PDA in neonate.
  3. Contraindications for indomethacin.
  4. Pharmacological closure of PDA—medication and dosage

Answer

  1. Tachypnea, tachycardia, RD, O, dependency, continuous murmur, child not gang weight, hyperdynamuc precordium, bounding pulses.

Cardiology 465


MNJ33-007
When examining a healthy 3-year-old boy during a health supervision visit, you hear a grade 2 systolic ejection murmur most clearly at the upper left sternal border:

  1. Differential diagnosis of ESM in second left ICS.
  2. Auscultatory findings in ASD
  3. Types of ASD.
  4. Children with ASD and moderate to severe pulmonary hypertension which associated conditions should be ruled out.

Answer

  1. ASD, increased PBF, AS, PS and CoA

MNJ33-008
Following an uncomplicated delivery, a3.7 kg term infant develops cyanosis in the first hour of life. Findings at 3 hours of age include: Cyanosis; heart rate: 140 beats/min; respiratory rate: 56 breaths/min; no heart murmurs; pulse oximetry in room air: 70% saturation in the right hand and 75% in the foot; in 100% FiO, via head-hood oxygen—saturation increases to 90% in the foot; chest radiography is normal:

  1. Clinical differentials.
  2. Describe hyperoxia test.
  3. Causes of differential cyanosis/reversed differential.

Answer

  1. Pre- and post-ductal oxygen saturations

Ans. 10.

Causes of sudden cardiac death in children
Structural/functional Electrical
Hypertrophic cardiomyopathy Long QT/short QT syndrome
Coronary artery anomalies Wolff-Parkinson-White syndrome
Aortic rupture/Marfan's syndrome Brugada syndrome
Dilated cardiomyopathy Congenital heart block
Myocarditis/endocarditis Catecholaminergic ventricular tachycardia
LVOT obstruction Primary pulmonary hypertension
Mitral valve prolapse Drugs/stimulants
Coronary artery atherosclerotic heart disease Commotio cordis
Arrhythmogenic RV cardiomyopathy
Postoperative congenital heart disease

MNJ33-009
A 14-year-old girl falls during a race. She is unconscious, cyanotic, and has no pulse, but spontaneously revives within seconds. Both patient and family histories are benign. Results of physical examination:

  1. Causes of sudden cardiac death in children.
  2. Appropriate tests been excluded.
  3. Arrhythmias associated with syncope.

Answer

No model answer in source material.


MNJ33-010
A healthy 8-month-old boy has had intermittent episodes of intense cyanosis of the hands, lower arms, and feet since birth. The infant appears alert and playful during the episodes. At other times, his arms and legs are pink but havea "mottled" appearance. Physical examination reveals no remarkable findings other than mottling of the extremities:

  1. Causes of episodic acrocyanosis
  2. Diagnostic tests for this child

Answer

  1. Episodic acrocyanosis of the hands and feet, episodic arrhythmia, methemoglobinemia, cyanotic spells, seizures.

MNJ33-011
A 14-year-old boy in your practice is followed periodically for bicuspid aortic valve. He presents to you with 3 weeks history of fatigue and off and on fever of 101°F:

0.13.
1 At what age ECG resembles an adult ECG
2 Tall P waves in lead II 1s defined as height more than mm.
3 Maximum P wave duration in children 1s seconds.
4 Maximum P wave duration in infants <12 months seconds.
5 PR interval—lower limit in less than 3 years seconds.
0.14.

A 12-year-old boy presented with acute onset pain in left iliac fossa, fever, vomiting. Preoperative ECG is shown:

Cardiology 467 |

images/MNJ-P-OSCE 33. CVS_page_4_Figure_1.jpeg

  1. What will you look for on physical examination?
  2. He has elevated WBC and ESR. What other test you will ask for?
  3. What organisms are likely to grow on culture?
  4. What treatment regime is ideal?
  5. What risk this boy has for sudden deterioration?
  6. Analyse the ECG.
  7. Mention likely malformations associated with this condition.

Answer

Infective endocarditis (rest answer see the Nelson).


MNJ33-012

  1. At what FiO; level, patient should be on continuous pulse oximetry?
  2. What are the causes of (external and internal) inaccurate SpO, readings?
  3. A child rescued from fire at school on admussion to PICU shows 100% SpO, on pulse oximeter Intensive care in charge still puts him on oxygen and orders ABG Why?
  4. Whats the oxygen carrying capacity of a child with SpO, of 97% and Hb of 10?
  5. What 1s the lowest "safe" level (normal Hb, etc.) of % saturation of oxygen, and the corresponding PaO,?
  6. What should be done when ambient light interferes with SpO, reading?
  7. When will you suspect "ductus dependent circulation" on day 1 of life (by use of pulse oxumeter)?

Answer

No model answer in source material.


MNJ33-013

  1. Principles of management of congestive cardiac failure
  2. What are the specific drugs used in the management of congestive cardiac failure?

Answer

No model answer in source material.


MNJ33-014
| 462 OSCE Clinical Pediatrics ]

images/MNJ-P-OSCE 33. CVS_page_4_Figure_17.jpeg

  1. Identify the abnormality in the ECG.
  2. What electrolyte abnormality can cause this?
  3. Why is it important to identify this rhythm disturbance?

Answer

  1. Prolonged QT interval.

Ans. 18. 1.T,2.T,3 T,4 F,5.1T,6.T

*neonates had right axis deviation due to nght ventricle dommance

Cardiology 467

Ans. 19. 1. F, 2 F, 3. F, 4. F


MNJ33-015
True/False

  1. Neonates have right axis deviation.

Answer

No model answer in source material.


MNJ33-016
True/False about fetal circulation

  1. Umbilical vein carry deoxygenated blood in placenta from fetus
  2. Blood from superior vena cava preferentially flow across foramen ovale in to nght atrium
  3. 45% of right ventricular outflow enter enters the lung via pulmonary arteries
  4. Descending aorta connected to pulmonary artery via ductus venosus

Answer

No model answer in source material.


MNJ33-017
A 13 years old girl present with 3 months history of palpitation. She is fit and well grown without any recent illness and medication history. She is very good student in class also. She feel her heart rate rising and comes gradually down after 3—4 hours. No history of chest pain, collapse. Her symptoms usually present in school hours. She is good plays and not having any problem while playing. Mother tell no member in our family had heart disease. You found normal physical and systemic examination and her BP is also normal.

  1. What 1s possible diagnosis
  2. What test you will do before sending her home
  3. Cause of potental life threatening syncope 1n childrens(wmite any 3)
  4. When you will refer a child with syncope to cardiologist.

Answer

  1. Physiological tachycardia associated with situation related stress

MNJ33-018
From each of following clinical scenario pick the most likely diagnosis from the list.

  1. A13 years old boy treated for rhabdomyosarcoma ay 4 years age and treated with full recovery. Now he has shortness of breath smce 6 month, on examination he looks tired with mcreased respiratory rate. He has gallop rhythm and raised JVP. X-ray chest showed cardiomegaly.
  2. A 15 years old boy with history of loss of appetite, off and on fever since 1 month. On examination you found muffed heart sound and low platelet count on blood test. His mother gave history recurrent rash over his face when she play cricket.
  3. A7 years old girl presented with swollen left knee after recovery form swollen ankle last week. She has fever and pink rash over his trunk. She gave history of sore throat last month. You ordered ECG and found first degree heart block.
    c. Rheumatic fever
    d. JIA
    e. SLE

Answer

  1. a. Anthracycline induced cardiomyopathy-need lifelong annual ECHO

MNJ33-019
Cardiac investigations-choose the best investigation for given scenarios

images/MNJ-P-OSCE 33. CVS_page_6_Picture_1.jpeg

  1. A3 years old boy came to you for URI, on examination you notices murmur which 1s soft systolic at right supraclavicular area and became louder on sitting.
  2. A12 years old boy with recurrent panic attacks with fast heart rate. On examination he has resting heart rate of 120/min. his systemic examination 1s normal.
  3. A6 years old boy who repaired for aortic stenosis at 18 month age, present with shortness of breath. On examination you found systolic murmur on aortic area.
    c. Cardiac catheter
    d. ECHO
    e. MRI thorax
    f. Stress test

Answer

  1. b. This patient has innocent murmur-venous hum only do ECG and reassure the parents.

MNJ33-020
Chest pain-choose the best diagnosis for given scenarios.

  1. Al? years old girl referred to you for 11 month history of recurrent chest pain. The pain episode i is localized to left side and does not radiate. She recovered after few minutes. She is well grown, active girl without any clinical finding on examination.
  2. A115 years old boy rushed in causality for sudden collapse while playing football match. In causality he was awake and describe a severe chest pain with sweating. This 1s his first episode of this type of symptoms. On examination you found ejection systolic murmur at right upper sterna area that is radiating to carotid area No other finding in examination
  3. A110 years old girl present to you for 3 weeks history of left side chest pai that increase on deep breathing. There is no history of cough, fever, trauma and palpitation. Her cardiovascular, respiratory and GI examination is normal On examination you found tenderness over 2nd costochondral junction
    a. Aortic stenosis
    c. Pericardial catch syndrome
    d. HOCM
    e. Costochondritis

Answer

  1. c. Pericardial catch syndrome-this is classical presentation-recurrent chest pain for few minute that increase on deep breathing

MNJ33-021
An 8 years old boy is due for a minor procedure in OT today. Anesthetist cannot feel his femoral pulse. Child is referred to you and on examination he is nor cyanosed nor clubbed at finger. His femoral pulse was absent with forceful apex with out any thrill. A 3/6 systolic murmur is present at upper left sternum with radiation at back between the scapula. X-ray and angiogram are given below.

images/MNJ-P-OSCE 33. CVS_page_6_Picture_16.jpeg
images/MNJ-P-OSCE 33. CVS_page_6_Picture_17.jpeg

  1. What 1s finding in X-ray and MR angiogram?
  2. What is diagnosis on the base of chmical and inveshigation findings?
  3. What what 1s syndrome associated with this?
  4. Whatis plan of further treatment?

Answer

  1. Rib notching (X-ray) with coarctation just beyond the left subclavian artery (Angio)